Analysis of the PINK1 gene in a large cohort of cases with Parkinson disease.

نویسندگان

  • Ekaterina Rogaeva
  • Janel Johnson
  • Anthony E Lang
  • Cindy Gulick
  • Katrina Gwinn-Hardy
  • Toshitaka Kawarai
  • Christine Sato
  • Angharad Morgan
  • John Werner
  • Robert Nussbaum
  • Agnes Petit
  • Michael S Okun
  • Aideen McInerney
  • Ronald Mandel
  • Justus L Groen
  • Hubert H Fernandez
  • Ron Postuma
  • Kelly D Foote
  • Shabnam Salehi-Rad
  • Yan Liang
  • Sharon Reimsnider
  • Anurag Tandon
  • John Hardy
  • Peter St George-Hyslop
  • Andrew B Singleton
چکیده

BACKGROUND Mutations in the PTEN-induced kinase (PINK1) gene located within the PARK6 locus on chromosome 1p35-p36 have recently been identified in patients with recessive early-onset Parkinson disease. OBJECTIVE To assess the prevalence of PINK1 mutations within a series of early- and late-onset Parkinson disease patients living in North America. DESIGN All coding exons of the PINK1 gene were sequenced in a series of 289 Parkinson disease patients and 80 neurologically normal control subjects; the mutation frequencies were evaluated in additional controls (100 white and 50 Filipino subjects). RESULTS We identified 27 variants, including the first reported compound heterozygous mutation (Glu240Lys and Leu489Pro) and a homozygous Leu347Pro mutation in 2 unrelated young-onset Parkinson disease patients. CONCLUSION Autosomal recessive mutations in PINK1 are a rare cause of young-onset Parkinson disease.

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عنوان ژورنال:
  • Archives of neurology

دوره 61 12  شماره 

صفحات  -

تاریخ انتشار 2004